Background: Congenital heart disease is the leading cause of death in infants related to birth defects and can cause chronic defects (1). The most common complication is pulmonary hypertension (PH). The worst manifestation of PAH is Eisenmenger syndrome. If it has manifested into Eisenmenger syndrome, the defect in CHD cannot be corrected (2,3). Research on the characteristics of PAH in CHD needs to be known for better treatment. Methods: This is a descriptive study in pediatric patients with acyanotic congenital heart disease. In this research we used medical records. Data analysis was carried out descriptively. Results: The results of this study showed that the prevalence of PAH was 7.08%, and most of the patients were toddlers (33 patients or 57.9%) and female (38 patients of 66.7%). The most common diagnosis of CHD lesions was ASD, found in 19 patients (33.3%). Most patients came with severe PAH conditions. Pharmacological therapy in the form of sildenafil was mostly given. The most common symptoms were shortness of breath and murmurs on physical examination. There was no relationship between intervention variables, pharmacological therapy, and mortality and between diagnosis of CHD and severity of PAH. Conclusion: Although the prevalence of PAH was not high in this study, the mortality rate was quite high. It is necessary to educate the parents of patients with congenital heart disease so that further complications can be prevented early on. It is also necessary to make services better to improve the nutritional status of patients. Pharmacological therapy and intervention measures need to be reviewed and improved to reduce mortality in patients.

acyanotic CHD

pediatric

Congenital Heart Disease

pulmonary hypertension

pulmonary arterial hypertension